A rare cause of monoatrophy: hirayama disease

Hirayama Disease is a benign disease of the lower motor neurons which is encountered mostly in young adults. This disease is extremely rare and characterized by the wasting and weakness of the distal upper extremities. In this paper, we present a 16 year- old female patient with the complaint of weakness and muscle wasting of the hands and forearms.

Nadir görülen bir monoatrofi nedeni: Hirayama hastalýðý

Hirayama Hastalýðý, genç erkeklerde daha sýk görülen benign bir alt motor nöron hastalýðýdýr. Son derece enderdir. Distal üst ekstremitelerde güçsüzlük ve kas erimesiyle karakterizedir. Bu makalede ellerinde ve ön kolunda güçsüzlük ve kaslarýnda erime yakýnmasý olan 16 yaþýnda kýz hasta sunulmuþtur.