Primary sclerosing cholangitis without jaundice in a seventeen years old male-case report

Primary sclerosing cholangitis is an idiopathic, chronic and progressive liver disease which takes place as the inflamation, fibrosis and obliteration of the intrahepatic and extrahepatic bile ducts. It most commonly occurs in young men about forties. Primary sclerosing cholangitis is usually associated with inflamatory bowel disease. Inflamatory bowel disease and primary sclerosing cholangitis are seen together in men twice as in women. But primary sclerosing cholangitis especially seens in women without another disease. Usually first symptoms are jaundice and pruritus. In this case, our subject is an 17 years old male who has abdominal pain but no other diseases.

Onyedi yaþýndaki erkek hastada iktersiz primer sklerozan kolanjit-olgu sunumu

Primer sklerozan kolanjit (PSK), karaciðer içi ve dýþý safra yollarýnda inflamasyon, fibrozis ve bunlarýn sonucu geli- þen darlýklarla ortaya çýkan, idiopatik, kronik ve ilerleyici özellikte bir kolestatik karaciðer hastalýðýdýr. Genellikle erkeklerde ve 40’lý yaþlarda ortaya çýkar. PSK’le birlikte en sýk görülen hastalýk inflamatuar barsak hastalýklarý (ÝBH)’dýr. PSK ve ÝBH birlikteliði erkeklerde 2 kat daha sýk iken, tek baþýna PSK kadýnlarda daha sýktýr. Genellikle sarýlýk ve kaþýntý ilk bulgularýdýr. Bu makalede, normalden farklý olarak, nadir görülen örneðiyle hafif þiddette karýn aðrýsýyla kliniðe baþvuran, 17 yaþýnda, beraberinde ek hastalýk bulunmayan erkek bir primer sklerozan kolanjit vakasýný sunmayý amaçladýk.